Diencephalic syndrome of infantile emaciation. Analysis of literature and report of further 3 cases.
نویسندگان
چکیده
our own 3 is presented. Boys are affected more frequently than girls (1-8 :1) and the onset is during the first 12 months of life in 92% of cases. The main clinical features are emaciation, overactivity, pleasant disposition, and above-average height. The natural course of the disease is variable. Treatment is by radiotherapy. Operative intervention, except to relieve intracranial hypertension, is not usually indicated.
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عنوان ژورنال:
- Archives of disease in childhood
دوره 47 253 شماره
صفحات -
تاریخ انتشار 1972